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Tafazzin蛋白抗體說明書
  • 品牌:上海莼試
  • 產(chǎn)地:進口、國產(chǎn)
  • 貨號:CS11448
  • 發(fā)布日期: 2019-01-16
  • 更新日期: 2025-03-19
產(chǎn)品詳請
產(chǎn)地 進口、國產(chǎn)
品牌 上海莼試
保存條件 Store at -20 °C
貨號 CS11448
應(yīng)用范圍 WB=1:100-500 ELISA=1:500-1000 IP=1:20-100 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500
CAS編號
抗體名 Anti-Tafazzin
克隆性
靶點 詳見說明書
適應(yīng)物種 詳見說明書
形態(tài) 詳見說明書
宿主 詳見說明書
亞型 IgG
標識物 詳見說明書
濃度 1mg/1ml%
免疫原 KLH conjugated synthetic peptide derived from human Tafazzin

技術(shù)外包服務(wù):

Tafazzin蛋白抗體說明書 分子生物學:質(zhì)粒抽提、PCR、Q-PCRRT-PCR、分子生物學:基因合成、引物合成、基因測序、載體構(gòu)建等

蛋白工程:原核、哺乳動物蛋白表達系統(tǒng)等

病毒包裝:腺病毒、慢病毒等

抗體工程:磁珠分選、病理染色、WB、ELISAIP、IF、IHC、FACS、Confocal等等

細胞工程:細胞表型分析(凋亡、增殖、周期、遷移、侵襲、修復、克隆形成)、細胞培養(yǎng)、細胞膜制備、穩(wěn)定細胞株構(gòu)建、細胞RNAi技術(shù)等等。

實驗流程:

Tafazzin蛋白抗體說明書 英文名稱  Anti-Tafazzin

中文名稱  Tafazzin蛋白抗體說明書 

     Barth syndrome; Cardiomyopathy dilated 3A (X linked); EFE2; Endocardial fibroelastosis 2; Protein G4.5; Tafazzin; TAZ; TAZ protein; TAZ protein; TAZ_HUMAN.

產(chǎn)品屬性:

      1mg/1ml

規(guī)   0.1ml/100μg 0.2ml/200μg

抗體來源  Rabbit

克隆類型   polyclonal

交叉反應(yīng)   Human

產(chǎn)品類型   一抗  

研究領(lǐng)域     信號轉(zhuǎn)導

蛋白分子量  predicted molecular weight: 33kDa 

       Lyophilized or Liquid

  KLH conjugated synthetic peptide derived from human Tafazzin

      IgG

純化方法   affinity purified by Protein A

   Preservative: 15mM Sodium Azide, Constituents: 1% BSA, 0.01M PBS, pH 7.4

Tafazzin蛋白抗體說明書 產(chǎn)品應(yīng)用   WB=1:100-500 ELISA=1:500-1000 IP=1:20-100 IHC-P=1:100-500 IHC-F=1:100-500 ICC=1:100-500 IF=1:100-500

(石蠟切片需做抗原修復) 

 not yet tested in other applications.

 optimal dilutions/concentrations should be determined by the end user.  

保存條件  Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. The lyophilized antibody is stable at room temperature for at least one month and for greater than a year when kept at -20°C. When reconstituted in sterile pH 7.4 0.01M PBS or diluent of antibody the antibody is stable for at least two weeks at 2-4 °C. 

Important Note  This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications. 

產(chǎn)品介紹 This gene encodes a protein that is expressed at high levels in cardiac and skeletal muscle. Mutations in this gene have been associated with a number of clinical disorders including Barth syndrome, dilated cardiomyopathy (DCM), hypertrophic DCM, endocardial fibroelastosis, and left ventricular noncompaction (LVNC). Multiple transcript variants encoding different isoforms have been described. A long form and a short form of each of these isoforms is produced; the short form lacks a hydrophobic leader sequence and may exist as a cytoplasmic protein rather than being membrane-bound. Other alternatively spliced transcripts have been described but the full-length nature of all these transcripts is not known.

Function : Some isoforms may be involved in cardiolipin (CL) metabolism.

Subcellular Location : Isoform 1: Membrane; Single-pass membrane protein.

Isoform 2: Cytoplasm (Probable).

Isoform 3: Membrane; Single-pass membrane protein.

Isoform 4: Membrane; Single-pass membrane protein.

Isoform 5: Membrane; Single-pass membrane protein.

Isoform 6: Cytoplasm (Probable).

Isoform 7: Membrane; Single-pass membrane protein.

Isoform 8: Cytoplasm (Probable).

Isoform 9: Cytoplasm (Probable).

Tissue Specificity : High levels in cardiac and skeletal muscle. Up to 10 isoforms can be present in different amounts in different tissues. Most isoforms are ubiquitous. Isoforms that lack the N-terminus are found in leukocytes and fibroblasts, but not in heart and skeletal muscle. Some forms appear restricted to cardiac and skeletal muscle or to leukocytes.

DISEASE : Barth syndrome (BTHS) [MIM:302060]: An X-linked disease characterized by dilated cardiomyopathy with endocardial fibroelastosis, a predominantly proximal skeletal myopathy, growth retardation, neutropenia, and organic aciduria, particularly excess of 3-methylglutaconic acid. Additional features include hypertrophic cardiomyopathy, isolated left ventricular non-compaction, ventricular arrhythmia, motor delay, poor appetite, fatigue and exercise intolerance, hypoglycemia, lactic acidosis, hyperammonemia, and dramatic late catch-up growth after growth delay throughout childhood. Note=The disease is caused by mutations affecting the gene represented in this entry.

Similarity : Belongs to the taffazin family.

Database links : UniProtKB/Swiss-Prot: Q16635.1

全、新、優(yōu)、品、好四大特點:

Tafazzin蛋白抗體說明書 全:公司提供上萬種產(chǎn)品,涵蓋了生物試劑,elisa試劑盒,標準品,培養(yǎng)基,原裝耗材,抗體、培養(yǎng)基、ATCC細胞等,基本上各種科研所需產(chǎn)品在我司都能找到。

新:產(chǎn)品更新速度較快,基本上每周都有新產(chǎn)品出現(xiàn)。

優(yōu):產(chǎn)品質(zhì)量好,投訴比較少。

好:我公司具有優(yōu)質(zhì)的技術(shù)團隊,產(chǎn)品一旦售出,實驗過程中遇到困難可提供在線技術(shù)咨詢。使您使用產(chǎn)品時沒有任何的后顧之憂。

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